Science and Research

Outcomes in Patients Receiving Treatment for Pulmonary Arterial Hypertension Associated With Repaired Congenital Heart Disease

BACKGROUND: Pulmonary arterial hypertension (PAH) is a common complication among patients with congenital heart disease (CHD). Despite advances in PAH treatment, evidence for the benefits of PAH therapies in CHD-PAH is limited. OBJECTIVES: This analysis aimed to evaluate outcomes in patients with repaired PAH-CHD receiving an approved PAH drug. METHODS: This was a pooled analysis including CHD-PAH patients whose CHD was repaired 

  • Krasuski, R. A.
  • Tobore, T.
  • Studer, S.
  • Jansa, P.
  • Sitbon, O.
  • Hoeper, M. M.
  • Channick, R.
  • Gaine, S.
  • Lang, I.
  • Chin, K.
  • Pulido, T.
  • Mehta, S.
  • Torbicki, A.
  • Sastry, B.
  • Tang, X.
  • McLaughlin, V.
  • Reardon, L. C.

Keywords

  • Compass-2
  • Griphon
  • Seraphin
  • congenital heart disease
  • pooled analysis
  • pulmonary arterial hypertension
Publication details
DOI: 10.1016/j.jacadv.2025.101626
Journal: JACC Adv
Pages: 101626 
Number: 3
Work Type: Original
Location: BREATH
Disease Area: PH
Partner / Member: MHH
Access-Number: 39999520

DZL Engagements

chevron-down